A Narrow Internal Auditory Canal with Duplication in a Patient with Congenital Sensorineural Hearing Loss
نویسندگان
چکیده
A narrow internal auditory canal (IAC) with duplication is a rare anomaly of the temporal bone. It is associated with congenital sensorineural hearing loss. Aplasia or hypoplasia of the vestibulocochlear nerve may cause the hearing loss. We present an unusual case of an isolated narrow IAC with duplication that was detected by a CT scan. In this case, the IAC was divided by a bony septum into an empty stenotic inferoposterior portion and a large anterosuperior portion containing the facial nerve that was clearly delineated on MRI.
منابع مشابه
A 46-Year-Old Woman with Unilateral Hearing Loss: A Recent Diagnosis of a Birth Condition
Cochlear nerve (CN) aplasia refers to the absence of a visible CN on oblique sagittal magnetic resonance images of the lateral aspect of the inner auditory canal (IAC). Magnetic resonance (MR) is the preferred technique in patients with sensorineural hearing loss and/or vertigo; however, computed tomography (CT) is used to evaluate the IAC or facial nerve canal. Three types of aplasia or hypopl...
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متن کاملThe Significance of a Hypoplastic Bony Canal for the Cochlear Nerve in Patients with Sensorineural Hearing Loss: CT and MRI Findings1
Department of Radiology, Otolaryngology-Head and Neck Surgery, Yonsei University Wonju College of Medicine, Wonju, Korea. Received September 3, 2003 ; Accepted February 13, 2004 Address reprint requests to : Ki-jun Sung, M.D., Department of Radiology, Wonju College of Medicine, Yonsei University, Wonju Christian Hospital, 162 Ilsan-dong, Wonju, Kangwon-do, 220-701, Korea, Tel. 82-33-741-1475 Fa...
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عنوان ژورنال:
دوره 9 شماره
صفحات -
تاریخ انتشار 2008